Pustular psoriasis is an uncommon form of psoriasis consisting of widespread pustules on an erythematous background, as shown in the image below. file6387 See Psoriasis: Manifestations, Management Options, and Mimics, a Critical Images slideshow, to help recognize the major psoriasis subtypes and distinguish them from other skin lesions. Keywords: Pustular psoriasis, Palmoplantar pustulosis, Subcorneal pustular dermatosis, Deficiency of IL-1 receptor antagonist (DIRA), PAPA syndrome, SAPHO syndrome. 5 weeks of age with fetal distress, pustular rash, joint swelling, oral lesions and pain with movement. Although systemic manifestations are uncommon in SAPHO syndrome, fever and moderate elevations in acute phase reactants may occur, and up to 10 of patients with SAPHO syndrome develop inflammatory bowel disease, most commonly after the onset of SAPHO symptoms46, 48, 53, 56. Baker and Ryan also noted that localized and generalized forms of pustular psoriasis could overlap with one another over time73. Up to 30 of these patients manifest by age 2 with psoriatic diaper rash. A skin biopsy may be required to confirm the diagnosis in severe or worrisome cases. Pustular psoriasis in infancy may be localized or generalized.
If an adult or child presents with an acquired predominantly scaly eruption, the most likely explanation is psoriasis, which is estimated to affect 1-4 of the population. The skin disease may present as one or other form of acute psoriasis, chronic psoriasis or localised to hands and feet. These subtypes may overlap. Generalised pustular psoriasis may be confused with:. This form of psoriasis is characterized by an acute generalized eruption of smaller round. 1 It encompasses a spectrum of disease with several clinically distinct subtypes.
We present two cases of Netherton syndrome mimicking pustular psoriasis and discuss potential pathomechanisms of clinical and histologic similarities between Netherton syndrome and pustular psoriasis and implications for management. Pustular psoriasis eruption with dabrafenib, a BRAF inhibitor. Generalized pustular psoriasis (GPP) is a severe inflammatory skin disease characterized by the presence of sterile pustules covering almost the entire body and systemic symptoms such as fever. Variably considered as a localized subtype of pustular psoriasis, palmoplantar pustulosis (PPP) is commonly treated with topical steroids, acitretin, and local phototherapy with oral or topical psoralen (PUVA). Fortunatley, erythrodermic psoriasis is relatively uncommon. According to the National Psoriasis Foundation, It is the least common type of psoriasis and may occur once or more during a lifetime in 1-2 of those with psoriasis. At an early age, the presentation of psoriasis may be atypical. Of particular interest, skin cancer was not detected in this series of children even after repeated courses.
Scaly Skin Diseases. Psoriasis Overview. Dermnet Nz
Although pediatric psoriasis is not uncommon, limited epidemiology data are available to date. Young children usually present with a diaper rash that is unresponsive to irritant diaper dermatitis treatment. Pustular psoriasis is characterized by localized or generalized superficial sterile pustules and can be accompanied by fever, malaise and arthralgias in the case of classical von Zumbusch type. Psoriasis of the skin can be accompanied by changes of the nail plate and nail bed. Prolonged pustular eruption from hydroxychloroquine: an unusual case of acute generalized exanthematous pustulosis. GPP may also present severe extracutaneous manifestations including pneumonitis, heart failure and hepatitis. Generalized pustular psoriasis (GPP) is a severe inflammatory skin disease characterized by the presence of sterile pustules covering almost the entire body and systemic symptoms such as fever. An Uncommon Side Effect of Bupropion: A Case of Acute Generalized Exanthematous Pustulosis. PSORIASIS VULGARIS (Most common subtype is chronic plaque psoriasis) 2. A. Generalized pustular psoriasis: Generalized pustular psoriasis during pregnancy is also referred to as impetigo herpetiformis. Lesions may appear at the Annular pustular psoriasis. It is rare sterile, pustular eruption distal portions of fingers or sometimes toes slowly extends proximally. Relatively uncommon. The free wiki textbook of skin conditions that dermatology professionals can edit. Abstract. Pustular psoriasis is an uncommon variant of psoriasis that is characterized by the presence of widespread, erythematous, sterile pustules. This subtype usually lacks systemic symptoms. The annular subtype is characterized by erythematous, annular lesions that have pustules at the advancing edge of a lesion and is associated with fever, malaise, and other systemic manifestations. Psoriasis glossary including various medical information. The condition may be inherited or may be acquired in occupations involving polyvinylcholoride plastic material. There are various subtypes of the disorder: generalized, annular, palmoplantar or juvenile. They found that the incidence of psoriasis among total skin patients ranged between 0. But even same clinical subtype can behave differently in different individuals. Certain clinical variants like erythroderma, localized and generalized pustular psoriasis and arthropathy are uncommon.
Pustular psoriasis can be localized, commonly to the hands and feet (palmoplantar pustulosis), or generalized with widespread patches occurring randomly on any part of the body. Generalized pustular psoriasis (pustular psoriasis of von Zumbusch), also known as impetigo herpetiformis during pregnancy, 19 is a rare and severe form of psoriasis that may require hospitalization. This skin eruption is often accompanied by a fever, muscle aches, nausea, and an elevated white blood cell count. Napkin psoriasis is a subtype of psoriasis common in infants characterized by red papules with silver scale in the diaper area that may extend to the torso or limbs.